Sturge-Weber syndrome: a report of 14 cases

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Abstract

Sturge-Weber-Krabe syndrome (SWS), alsoknown as encephalotrigeminalangiomatosisand named the forthfacomatosis, recall thenames of the authors who first describedit inits basic clinical, radiological andanatomopathologicalaspects. We report here 14cases of Sturge-Weber disease. In 6 of these,despite what had been previously described inliterature, an extension of the angioma hasbeen noted in other parts of the body. Thestudy of these subjects stresses not only theneed for a pharmacological/neuropsychomotorintervention, but alsothe need of a psychotherapeuticapproach, for the emotional and affectiveimplications thatcould derive from thissyndrome. The reported cases are similar tothose presented in literature for their mainfeatures. In particular, two elements are interesting:i) the exceptional diffusion of the rednevousto the whole hemicorpo; and ii) theevaluation of the way the patients live the disease,which has not beenpreviously consideredin literature. We can conclude that SWS is amultisystem disorder that requires the neurologistto be aware of the possible endocrine,psychiatric, ophthalmological, and other medicalissues that can arise and impact on theneurological status of the patients.and neuropsychomotor therapies,but also a psychotherapeutic support topatients. It should be noted that the literaturedoes not take psychotherapeutic support intoconsideration.
Lingua originaleEnglish
pagine (da-a)26-28
Numero di pagine3
RivistaMental Illness
Volume5
Stato di pubblicazionePublished - 2013

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