INSUFFICIENZA CARDIACA ACUTA E CARDIOMIOPATIE: UN CASO CLINICO

Isolated noncompaction of left ventricular myocardium is a rare congenital heart disease, characterizedby an excessive prominence of trabecular meshwork, spaced out by deep intertrabecular recesses,consequent to the arrest of the normal myocardial embryogenesis. Although there are numerousdescriptions, the pathophysiological effects of the structural alterations, like the clinical spectrum andthe evolution of the disease, are not fully clarified.In this paper we evaluated the natural history of the disease, the family incidence and the alterationsof the systolic and diastolic function. An interesting case report is described concerning a patientaffected by noncompaction and atrial fibrillation